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人类医学对遗传性心律失常的认识始于1957年。那年,Jervell与同事Lange-Nielsen首次报告了伴有耳聋的家族性LQTS病例,随后其被命名为Jervell-Lange-Nielsen(JLN)综合征。6年后的1963年,Romano和Ward分别报告了不伴耳聋而听力完全正常的LQTS。30年后的1993年,Schwartz等代表国际LQTS协作组提出了LQTS的诊断标准。至此,做为心律失常领域的一个新分支,遗传性心律失常展现于世。更让人眼前一亮的是,70多年来,遗传性心律失常领域的迅猛发展,让人眼花缭乱,给人日新月异的感觉。该领域的快速发展,可用世人常用的一个成语概括之:魔高一尺,道高一丈。
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PérezRiera Andrés Ricardo,BarbosaBarros Raimundo,Andreou Andreas Y,FiolSala Miguel,Birnbaum Yochai,Silva Rocha Maurício da,DaminelloRaimundo Rodrigo,Abreu Luiz Carlos de,Nikus Kjell.Left Septal Fascicular Block: Evidence, causes, and diagnostic criteria.[J].Heart rhythm,2023.
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Coluccia Giovanni,Oddone Daniele,Maggi Roberto,Corallo Serena,Senes Jacopo,Donateo Paolo,Puggioni Enrico,Brignole Michele.Left bundle branch area pacing in a young athlete with progressive cardiac conduction (Lev-Lenegre) disease[J].Journal of Electrocardiology,2021.
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